DM1 (n = 112) | Controls (n = 50) | p value | ||
---|---|---|---|---|
Clinical characteristics | Age, mean (IQR) | 44.3 (36–53) | 45.7 (38–53) | 0.49a |
Sex, female (%) | 48 (43) | 26 (52) | 0.31b | |
DM1 related factors | CTG repeat numbers, mean (IQR) | 950 (600–1366) | NA | NA |
Imaging characteristics | z-Evans Index, mean (IQR) | 0.29 (0.27–0.32) | 0.24 (0.23–0.26) | < .01a |
Callosal angle, mean (IQR) | 123 (115–129) | 123 (112–127) | 0.83a | |
Sylvian fissure dilation, n (%) | 61 (54) | 2 (4) | < .01b | |
High-convexity tightness, n (%) | 9 (8) | 0 (0) | 0.06b | |
CS-EPVS, n (%) | 35 (31) | 9 (18) | 0.09b | |
Temporo-polar WMH, n (%) | 82 (73) | 0 (0) | < .01b | |
Pathological brain atrophy, n (%) | 46 (41) | 1 (2) | < .01b |