Fig. 4

The proportion of imaging features for each age group of DM1 patients. Age-group A: ≤ 39 years old. Age-group B: 40–49 years old. Age-group C: ≥ 50 years old. A z-Evans Index of > 0.3 was defined as ventriculomegaly. For the subjective scale of high-convexity tightness and Sylvian fissure dilation, “2 or 3” was considered a pathologic finding. Thus, high-convexity tightness (2 or 3) combined with Sylvian fissure dilation (2 or 3) accompanied by ventriculomegaly was defined as disproportionately enlarged subarachnoid space hydrocephalus (DESH)